氨基己糖苷酶Aα(HEXa)重组蛋白

Recombinant Hexosaminidase A Alpha (HEXa)

TSD; Hex-A; Tay Sachs Disease; GM2 Gangliosidosis; Beta-Hexosaminidase Subunit Alpha; Beta-N-Acetylhexosaminidase Subunit Alpha; N-Acetyl-Beta-Glucosaminidase Alpha

序列

用法

Reconstitute in 10mM PBS (pH7.4) to a concentration of 0.1-1.0 mg/mL. Do not vortex.

储存

避免反复冻融。2-8°C不超过一个月,-80°C不超过12个月。

稳定性

热稳定性以损失率显示。损失率是由加速降解试验决定,具体方法如下:在37°C孵育48小时,没有显著的降解或者沉淀产生。保质期内,在适当的条件下存储,损失率低于5%。

相关产品

编号适用物种:Homo sapiens (Human,人)应用(仅供研究使用,不用于临床诊断!)
RPA195Hu01氨基己糖苷酶Aα(HEXa)重组蛋白Positive Control; Immunogen; SDS-PAGE; WB.
PAA195Hu01氨基己糖苷酶Aα(HEXa)多克隆抗体WB
MAA195Hu22氨基己糖苷酶Aα(HEXa)单克隆抗体WB; IHC; ICC; IP.
SEA195Hu氨基己糖苷酶Aα(HEXa)检测试剂盒(酶联免疫吸附试验法)Enzyme-linked immunosorbent assay for Antigen Detection.
LMA195Hu氨基己糖苷酶Aα(HEXa)等多因子检测试剂盒(流式荧光发光法)FLIA Kit for Antigen Detection.

参考文献

杂志参考文献
Neural Regen ResFunctionality of a bicistronic construction containing HEXA and HEXB genes encoding ¦Â-hexosaminidase A for cell-mediated therapy of GM2 gangliosidoses[34100447]
lifeSerum Cytokine Profile, Beta-Hexosaminidase A Enzymatic Activity and GM2 Ganglioside Levels in the Plasma of a Tay-Sachs Disease Patient after Cord Blood Cell …[34685379]